Eisemnengerís syndrome


It occurs in about 20 % of cases of shunt esp. V.S.D.
the development of this syndrome is genetically determined due to persistence of the fetal pattern of the pulm arterioles (abnormal muscle fibres)
C/P
Cyanosis - Clubbing
P++
Į C.O.P.
signs of P++ pulsations
dullness
S2
­ (P++)

Investigations
1. X-ray P++
2. E.C.G. P- pulmonale
Treatment

Surgery is of no value as the shunt acts as a safety valve.
Heart & lung transplantation . ?!

Source: Internal Medicine Book of Dr.Osama Mahmoud (Ain Shams University)