Ebstein’s Anomaly

Huge Rt. atrium Cyanosis
A rare anomaly of the tricuspid valve in which the post. leaflet of the
valve is attached lower down to the mass of the Rt. V. T.I.
s Rt. atrium hugely ++
s Central cyanosis result from blood shunting through A.S.D.
C/Pcentral cyanosis since birth
Treatment valve replacement & closure of A.S.D.
Atr. ++
i.e. Atrialization cyanosis
of the Rt. V.

Source: Internal Medicine Book of Dr.Osama Mahmoud (Ain Shams University)