View Full Version : Cysticfibrosis (mucoviscidosis)Or congenital polycyst ( Causes - C/P - Investigations - Treatment )

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03-18-2009, 10:39 AM
Cysticfibrosis (mucoviscidosis)
Or congenital polycystic lung
Its an inherited disease affecting exocrine gland.(A.R)
Viscid mucus obstruction Cystic dilatation with infection.
I- polycystic lung (this is the target organ of this systemic disease), it gives picture as bronchiectasis

+ Extrapulmonary. manifestations.

Meconium infertility cystic paucciaze liver
viscid secretion malabsorption biliaty cirrhosis
of prostate &cervix,
obstruction of vas deference
Investigations X-ray soap bubbles
Pancreatic function
NaCl in sweat is increased
Treatment 1- As bronchiectasis
2- Replacement therapy for pancreatic diseases
(pancreatic enzymes)

Source: Internal Medicine Book of Dr.Osama Mahmoud (Ain Shams University)